Case of the Month #17 - Haemophagocytic Lymphohistiocytosis (HLH)

Published 01/02/2022

What is the treatment?

The management of HLH involves prompt diagnosis, supportive therapy, treatment of any potential triggers and rapid immunosuppression to dampen the damaging ‘cytokine storm’2.  Specific treatment includes:

  1. Steroids or ciclosporin
  2. IV immunoglobulin
  3. Plasma exchange
  4. Biological therapies